RESUMO
Several patients suffer from rib fractures after traumas, and in severe cases it can be life-threatening. Until recently, attempts to perform surgical fixation in patients with instability have been unsuccessful. Chronic non-union causes persistent pain, disability and loss of quality of life. Implementation of surgical stabilization of rib fractures with tailored plates seems to improve pain relief, especially in cases of non-union but also in patients with instability of the chest wall after severe traumas, where advanced pain treatment (epidural catheter) is insufficient or weaning off fails.
Assuntos
Tórax Fundido/cirurgia , Fixação Interna de Fraturas/métodos , Pseudoartrose/cirurgia , Fraturas das Costelas/cirurgia , Parede Torácica/cirurgia , Analgesia Epidural , Placas Ósseas , Humanos , Imageamento Tridimensional , Dor/tratamento farmacológico , Manejo da Dor , Pseudoartrose/diagnóstico por imagem , Pseudoartrose/patologia , Radiografia , Fraturas das Costelas/diagnóstico por imagem , Fraturas das Costelas/patologia , Parede Torácica/diagnóstico por imagem , Parede Torácica/lesões , Parede Torácica/patologia , Titânio , Tomografia Computadorizada por Raios XRESUMO
Congenital central hypoventilation syndrome (CCHS) is a rare multisystem disorder characterized by autonomic nervous system dysfunction, which often manifests as failure to maintain ventilatory homeostasis during sleep. We present a case with a third degree atrioventricular block in a young woman with CCHS, which to our knowledge has not been seen before. As sudden death is known to occur among patients with CCHS, and it is under consideration to offer regularly monitoring of patients throughout childhood and adolescence.